|
|   |
306900
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|   |
000539
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|   |
emerg
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240
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5561
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D002836
|
(also spelled '''Hemophilia B''' or '''Hæmophilia B''') is a 1952;2:1378-1382. PMID 12997790.
Treatment (bleeding prophylaxis) is by intravenous infusion of factor IX.
The factor IX gene is located on the
X Chromosome (Xq27.1-q27.2). It is inherited
X-linked recessive, which explains why - as in haemophilia A - mostly males are generally affected.
Factor IX deficiency leads to an increased propensity for
Haemorrhage . This is in response to mild trauma or even spontaneously, such as in joints (
Haemarthrosis ) or muscles.