Sturge-weber Syndrome Website Links For
Syndrome
 

Information About

Sturge-weber Syndrome




  Name Sturge-Weber syndrome
  ICD10 Q858
  ICD9


Sturge-Weber syndrome, sometimes referred to as Encephalotrigeminal Angiomatosis , is an extremely rare Congenital neurocutaneous disorder. It is one of the Phakomatoses and is often associated with Port-wine Stain s of the face, Glaucoma , Seizures , Mental Retardation , and Ipsilateral Leptomeningeal Angioma .

It is an embryonal developmental anomaly of Mesoderm al and Ectoderm al development.

Unlike other neurocutaneous disorders ( Phakomatoses ), Sturge-Weber does not have a hereditary tendency but occurs sporadically.


EXTERNAL LINKS